Search results for " Schoenlein-Henoch"

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NON SOLO PORPORA… SUCCESSO DELLA STRATEGIA TERAPEUTICA E NUTRIZIONALE

2018

La porpora di Schoenlein-Henoch (HSP) è la vasculite più comune in età pediatrica caratterizzata da depositi di immunocomplessi di IgA nei piccoli vasi. L’eziologia non è nota, ma è possibile una correlazione con infezioni batteriche, virus, alimentazione, punture di insetti e agenti fisici. La diagnosi è principalmente clinica. Le principali manifestazioni sono porpora cutanea, artrite, manifestazioni gastrointestinali e nefrite. Manifestazioni neurologiche e cardiache sono rare, come le localizzazioni polmonari e testicolari. Sporadicamente è descritto un coinvolgimento pancreatico. Riportiamo il caso di un bambino di 5 anni con HSP ad interessamento pluridistrettuale. B.G. giunge alla no…

Settore MED/38 - Pediatria Generale E Specialisticaporpora di Schoenlein-Henoch strategia nutrizionaleporpora di Schoenlein-Henochstrategia nutrizionale
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EULAR/PRINTO/PRES criteria for Henoch-Schonlein purpura, childhood polyarteritis nodosa, childhood Wegener granulomatosis and childhood Takayasu arte…

2010

EULAR/PRINTO/PRES Objectives To validate the previously proposed classification criteria for Henoch-Schonlein purpura (HSP), childhood polyarteritis nodosa (c-PAN), c-Wegener granulomatosis (c-WG) and c-Takayasu arteritis (c-TA).Methods Step 1: retrospective/prospective webdata collection for children with HSP, c-PAN, c-WG and c-TA with age at diagnosis <= 18 years. Step 2: blinded classification by consensus panel of a representative sample of 280 cases. Step 3: statistical (sensitivity, specificity, area under the curve and.-agreement) and nominal group technique consensus evaluations.Results 827 patients with HSP, 150 with c-PAN, 60 with c-WG, 87 with c-TA and 52 with c-other were compar…

Genetics and Molecular Biology (all)myalgiaVasculitismedicine.medical_specialtyHenoch-Schonlein purpuraAdolescentIgA VasculitisClassification criteriaInternational CooperationImmunologychildhood polyarteritis nodosaBiochemistryGeneral Biochemistry Genetics and Molecular BiologyRheumatologyhemic and lymphatic diseasesTerminology as TopicSchoenlein-HenochmedicineHumansImmunology and Allergycardiovascular diseasesArteritisChildPurpurac-Wegener granulomatosisAdolescent; Child; Epidemiologic Methods; Granulomatosis with Polyangiitis; Humans; International Cooperation; Polyarteritis Nodosa; Purpura Schoenlein-Henoch; Takayasu Arteritis; Terminology as Topic; Rheumatology; Immunology; Biochemistry Genetics and Molecular Biology (all); Immunology and Allergycriteria; children; Henoch-Schönlein purpura; childhood polyarteritis nodosa; Wegener granulomatosis; Takayasu arteritis; EULAR; PRINTO; PRESPolyarteritis nodosabusiness.industryGranulomatosis with Polyangiitismedicine.diseaseTakayasu ArteritisDermatologyPolyarteritis NodosaSurgeryHenoch-Schönlein purpuraIgA vasculitisSettore MED/38 - PEDIATRIA GENERALE E SPECIALISTICAmedicine.symptomEpidemiologic MethodsGranulomatosis with polyangiitisVasculitisbusinessRheumatismc-Takayasu arteriti
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